الثلاثاء، 28 أغسطس 2018

277-Marfan Syndrome

About
Genetically inherited disorder causing abnormalities of several body components including bone, eyes, cardiac, and central nervous system.
Assess
Very tall with long hands and feet; mitral valve problems, visual difficulties; lateral curvature of the spine, skeletal abnormalities.
Complications
Cardiac problems- aortic rupture or aneurysm, mitral valve prolapse
Visual disturbances
Diagnosis
  • Disturbed sensory perception related to visual disturbances associated with disease process
  • Decreased cardiac output related to cardiac defects associated with disease
Goals
The client will remain free from injury.
Interventions
  • Administer medications, including cardiovascular medications, as ordered to manage disease manifestations.
  • Teach client about the disease.
  • Encourage genetic counseling if planning to conceive a child.
  • Teach client to continue close follow-up as indicated.
  • Prepare for orthopedic surgery, if indicated.
  • Monitor for signs/ symptoms of complications.

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